A pigmented hairy nevus with limb reduction
How to cite this article: Sangwan P, Thakur V. A pigmented hairy nevus with limb reduction. CosmoDerma 2023;3:148.
A 16-year-old boy presented with a brown flat lesion over the left upper back for 5–6 years. On examination, an ill-defined hyperpigmented patch of size 10 × 10 cm with hypertrichosis was present over the left scapular area and extending onto the left arm [Figure 1]. In addition, the left upper limb was shortened in length since birth and thoracic scoliosis was noted [Figure 2]. Hence, a diagnosis of Becker’s nevus syndrome (BNS) was made clinically and on investigating further, an X-ray spine showed thoracic scoliosis, rest being normal. The patient was counseled regarding the disease and referred to orthopedics for further management.
BNS is an epidermal nevus characterized by hyperpigmentation, hypertrichosis, and hamartomatous increase of smooth muscle fibers associated with various developmental defects including ipsilateral limb reduction as highlighted in this case.
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