Generic selectors
Exact matches only
Search in title
Search in content
Post Type Selectors
Filter by Categories
Brief Report
Case Report
Editorial
Focus
Images/Instrument in Dermatology/Dermatosurgery
Innovations
Letter to the Editor
Living Legends
Looking back in history
Original Article
Perspective
Resident Forum
Review Article
Spot the Diagnosis
Tropical Dermatology
Visual Treats in Dermatology
Generic selectors
Exact matches only
Search in title
Search in content
Post Type Selectors
Filter by Categories
Brief Report
Case Report
Editorial
Focus
Images/Instrument in Dermatology/Dermatosurgery
Innovations
Letter to the Editor
Living Legends
Looking back in history
Original Article
Perspective
Resident Forum
Review Article
Spot the Diagnosis
Tropical Dermatology
Visual Treats in Dermatology
Generic selectors
Exact matches only
Search in title
Search in content
Post Type Selectors
Filter by Categories
Brief Report
Case Report
Editorial
Focus
Images/Instrument in Dermatology/Dermatosurgery
Innovations
Letter to the Editor
Living Legends
Looking back in history
Original Article
Perspective
Resident Forum
Review Article
Spot the Diagnosis
Tropical Dermatology
Visual Treats in Dermatology
View/Download PDF

Translate this page into:

Visual Treats in Dermatology
2023
:3;
148
doi:
10.25259/CSDM_138_2023

A pigmented hairy nevus with limb reduction

Department of Dermatology, Venereology and Leprosy, AIIMS, Bhubaneswar, Odisha, India
Corresponding author: Vishal Thakur, Department of Dermatology, Venereology and Leprosy, AIIMS, Bhubaneswar, Odisha, India. drvishal87igmc@gmail.com
Licence
This is an open-access article distributed under the terms of the Creative Commons Attribution-Non Commercial-Share Alike 4.0 License, which allows others to remix, transform, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms.

How to cite this article: Sangwan P, Thakur V. A pigmented hairy nevus with limb reduction. CosmoDerma 2023;3:148.

A 16-year-old boy presented with a brown flat lesion over the left upper back for 5–6 years. On examination, an ill-defined hyperpigmented patch of size 10 × 10 cm with hypertrichosis was present over the left scapular area and extending onto the left arm [Figure 1]. In addition, the left upper limb was shortened in length since birth and thoracic scoliosis was noted [Figure 2]. Hence, a diagnosis of Becker’s nevus syndrome (BNS) was made clinically and on investigating further, an X-ray spine showed thoracic scoliosis, rest being normal. The patient was counseled regarding the disease and referred to orthopedics for further management.

Figure 1:
Clinical image of lesion over back showing ill-defined hyperpigmented patch of size 10 × 10 cm with hypertrichosis over the left scapular area and extending onto the left arm. In addition, the left upper limb is shortened in length with notable thoracic scoliosis.
Figure 2:
Clinical image of patient showing shortening of the left upper limb and thoracic scoliosis.

BNS is an epidermal nevus characterized by hyperpigmentation, hypertrichosis, and hamartomatous increase of smooth muscle fibers associated with various developmental defects including ipsilateral limb reduction as highlighted in this case.[1]

Declaration of patient consent

The authors certify that they have obtained all appropriate patient consent.

Conflicts of interest

There are no conflicts of interest

Use of artificial intelligence (AI)-assisted technology for manuscript preparation

The authors confirm that there was no use of artificial intelligence (AI)-assisted technology for assisting in the writing or editing of the manuscript and no images were manipulated using AI.

Financial support and sponsorship

Nil.

References

  1. , . Becker nevus syndrome. Am J Med Genet. 1997;68:357-61.
    [CrossRef] [Google Scholar]

Fulltext Views
1,255

PDF downloads
2,431
View/Download PDF
Download Citations
BibTeX
RIS
Show Sections